RIGI

RNA sensor RIG-I
OMIM: 609631, ClinGen, DECIPHER

4 panels

Panel Reviews Mode of inheritance Details
4 panels

Green RIGI in Glaucoma congenital


Level 2: Ophthalmological disorders
Version 2.0

2 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Expert list
Phenotypes
  • Singleton-Merten syndrome 2, MIM# 616298

Green RIGI in Mendeliome


Version 2.0

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • Singleton-Merten syndrome 2, MIM# 616298
Tags
  • new gene name

Green RIGI in Autoinflammatory Disorders


Level 2: Immunological disorders
Version 3.0

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • Lupus Nephritis, MONDO:0005556, DDX58-related

Green RIGI in Immune_markers_WTS_UMCCR


Level 2: Cancer
Version 1.0

0 reviews Unknown
Sources
  • Expert list
  • Expert Review Green
Tags
  • umccr