TSEN34:Ensemblv115

tRNA splicing endonuclease subunit 34
OMIM: 608754, ClinGen, DECIPHER

1 panel

Panel Reviews Mode of inheritance Details
1 panel

Red TSEN34 in Cerebellar and Pontocerebellar Hypoplasia


Level 2: Neurology and neurodevelopmental disorders
Version 2.0

1 review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Victorian Clinical Genetics Services
  • Expert Review Red
Phenotypes
  • Pontocerebellar hypoplasia type 2C, MIM# 612390