STING1

stimulator of interferon response cGAMP interactor 1
OMIM: 612374, ClinGen, DECIPHER

6 panels

Panel Reviews Mode of inheritance Details
6 panels

Green STING1 in Vasculitis


Level 2: Immunological disorders
Version 1.0

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Victorian Clinical Genetics Services
  • Expert Review Green
Phenotypes
  • STING-associated vasculopathy, infantile-onset, MIM# 615934

Green STING1 in Interstitial Lung Disease


Level 2: Respiratory disorders
Version 2.0

2 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Victorian Clinical Genetics Services
  • Expert Review
  • Expert Review Green
Phenotypes
  • STING-associated vasculopathy, infantile-onset, MIM# 615934
Tags
  • new gene name

Green STING1 in Pulmonary Fibrosis_Interstitial Lung Disease


Level 2: Respiratory disorders
Version 1.0

2 reviews BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review
  • Expert Review Green
Phenotypes
  • STING-associated vasculopathy, infantile-onset, MIM# 615934

Green STING1 in Disorders of immune dysregulation


Level 2: Immunological disorders
Version 2.0

1 review Unknown
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
  • Melbourne Genomics Health Alliance Immunology Flagship
  • Expert list
  • Expert Review Green

Green STING1 in Autoinflammatory Disorders


Level 2: Immunological disorders
Version 3.0

2 reviews BOTH monoallelic and biallelic, autosomal or pseudoautosomal
Sources
  • Expert list
  • Expert Review Green
Phenotypes
  • STING-associated vasculopathy, infantile-onset, MIM# 615934

Green STING1 in Nucleotide metabolism disorders


Level 2: Metabolic disorders
Version 1.0

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Victorian Clinical Genetics Services
  • Expert Review Green
  • Expert Review Green
Phenotypes
  • STING-associated vasculopathy with onset in infancy MONDO:0014405