PMVK

phosphomevalonate kinase
OMIM: 607622, ClinGen, DECIPHER

4 panels

Panel Reviews Mode of inheritance Details
4 panels

Green PMVK in Ichthyosis and Porokeratosis


Level 2: Dermatological disorders
Version 2.0

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • porokeratosis 1, Mibelli type MONDO:0008290

Green PMVK in Mendeliome


Version 2.0

1 review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Expert Review
Phenotypes
  • Porokeratosis 1, multiple types, MIM# 175800
  • Autoinflammatory syndrome, MONDO:0019751, PMVK-related

Green PMVK in Autoinflammatory Disorders


Level 2: Immunological disorders
Version 3.0

2 reviews BOTH monoallelic and biallelic (but BIALLELIC mutations cause a more SEVERE disease form), autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Literature
  • Literature
Phenotypes
  • Autoinflammatory syndrome, MONDO:0019751, PMVK-related

Amber PMVK in Mosaic skin disorders


Level 2: Dermatological disorders
Version 2.0

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Amber
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Linear porokeratosis
  • Porokeratosis 1, multiple types, MIM# 175800