NSMCE2

NSE2 SUMO ligase component of SMC5/6 complex
OMIM: 617246, ClinGen, DECIPHER

4 panels

Panel Reviews Mode of inheritance Details
4 panels

Amber NSMCE2 in Mendeliome


Version 2.0

2 reviews BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Amber
  • Literature
Phenotypes
  • Seckel syndrome 10, MONDO:0014991

Amber NSMCE2 in Microcephaly


Level 2: Dysmorphic and congenital abnormality syndromes
Version 2.0

2 reviews BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Amber
  • Literature
Phenotypes
  • Seckel syndrome 10, MONDO:0014991

Amber NSMCE2 in Monogenic Diabetes


Level 2: Endocrine disorders
Version 1.0

Component of the following Super Panels:

  • Metabolic Disorders Superpanel
  • 2 reviews BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Amber
    • Literature
    • Literature
    Phenotypes
    • Seckel syndrome 10, MONDO:0014991

    Amber NSMCE2 in Growth failure


    Version 2.0

    2 reviews BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Amber
    • Literature
    • Literature
    Phenotypes
    • Seckel syndrome 10, MONDO:0014991