MT-TN

mitochondrially encoded tRNA-Asn (AAU/C)
OMIM: 590010, ClinGen, DECIPHER

3 panels

Panel Reviews Mode of inheritance Details
3 panels

Green MT-TN in Mitochondrial disease


Level 2: Metabolic disorders
Version 2.0

Component of the following Super Panels:

  • Metabolic Disorders Superpanel
  • Progressive Neurological Conditions
  • 1 review MITOCHONDRIAL
    Sources
    • Expert Review Green
    • Expert list
    Phenotypes
    • mitochondrial disease MONDO:0044970, MT-TN related

    Green MT-TN in Hereditary Neuropathy


    Level 2: Neurology and neurodevelopmental disorders
    Version 2.0

    Component of the following Super Panels:

  • Neuromuscular Superpanel
  • Progressive Neurological Conditions
  • 1 review MITOCHONDRIAL
    Sources
    • Expert Review Green
    • Expert list
    • Expert list
    Phenotypes
    • mitochondrial disease MONDO:0044970, MT-TN related

    Green MT-TN in Rhabdomyolysis and Metabolic Myopathy


    Level 2: Neurology and neurodevelopmental disorders
    Version 2.0

    Component of the following Super Panels:

  • Myopathy Superpanel
  • Neuromuscular Superpanel
  • Progressive Neurological Conditions
  • 1 review MITOCHONDRIAL
    Sources
    • Expert Review Green
    • Expert list
    • Expert list
    Phenotypes
    • mitochondrial disease MONDO:0044970, MT-TN related