DGCR8:Ensemblv90

DGCR8, microprocessor complex subunit
OMIM: 609030, ClinGen, DECIPHER

3 panels

Panel Reviews Mode of inheritance Details
3 panels

Red DGCR8 in Mendeliome


Version 1.3802

3 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert list
  • Expert Review Red
Phenotypes
  • Schwannoma, MONDO:0002546
  • Early-onset multinodular goiter and schwannomatosis, no MIM#

Red DGCR8 in Schwannomatosis


Level 2: Neurology and neurodevelopmental disorders
Version 0.17

2 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Red
  • Literature
Phenotypes
  • Early-onset multinodular goiter and schwannomatosis

Red DGCR8 in Schwannomatosis


Level 2: Neurology and neurodevelopmental disorders
Version 1.0

2 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Literature
  • Expert Review Red
Phenotypes
  • Early-onset multinodular goiter and schwannomatosis