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Fetal anomalies v2.0 GNPNAT1 Gene migrated from ENSG00000100522 to ENSG00000100522 (gene set migration)
Fetal anomalies v1.567 GNPNAT1 Zornitza Stark Publications for gene: GNPNAT1 were set to 36097642; 35427807; 32591345
Fetal anomalies v1.566 GNPNAT1 Zornitza Stark Classified gene: GNPNAT1 as Green List (high evidence)
Fetal anomalies v1.566 GNPNAT1 Zornitza Stark Gene: gnpnat1 has been classified as Green List (High Evidence).
Fetal anomalies v1.565 Zornitza Stark Added reviews for gene GNPNAT1 from panel Skeletal dysplasia
Fetal anomalies v1.147 GNPNAT1 Zornitza Stark Marked gene: GNPNAT1 as ready
Fetal anomalies v1.147 GNPNAT1 Zornitza Stark Gene: gnpnat1 has been classified as Amber List (Moderate Evidence).
Fetal anomalies v1.147 GNPNAT1 Zornitza Stark Classified gene: GNPNAT1 as Amber List (moderate evidence)
Fetal anomalies v1.147 GNPNAT1 Zornitza Stark Gene: gnpnat1 has been classified as Amber List (Moderate Evidence).
Fetal anomalies v1.146 GNPNAT1 Zornitza Stark gene: GNPNAT1 was added
gene: GNPNAT1 was added to Fetal anomalies. Sources: Expert Review
Mode of inheritance for gene: GNPNAT1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: GNPNAT1 were set to 36097642; 35427807; 32591345
Phenotypes for gene: GNPNAT1 were set to Rhizomelic dysplasia, Ain-Naz type, MIM#619598
Review for gene: GNPNAT1 was set to AMBER
Added comment: 3 unrelated families reported with a skeletal dysplasia characterised by severe short stature and rhizomelic shortening. No antenatal features reported. The parents in PMID 36097642 had a medical termination of pregnancy at 4 months gestation for a fetus with skeletal anomalies - not genotyped.
Sources: Expert Review