Description
This panel contains genes that cause skin disorders as a result of somatic mutations and is suitable for use when affected tissue is being tested.

Please also refer to the Vascular Malformations_Somatic and Vascular Malformations_Germline panels for genes associated predominantly with vascular malformations of the skin.

With thanks to Genomics England PanelApp for the original design of this panel.

2 reviewers

  • Zornitza Stark (Victorian Clinical Genetics Services)

  • Mathew Wallis (Tasmanian Clinical Genetics Service)

6 Entities

reviewed, green

List Entity Reviews Mode of inheritance Details
6 Entitiess
Green Green List (high evidence)
AKT1
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Proteus syndrome, somatic 176920
Tags
  • somatic
Green Green List (high evidence)
FGFR1
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Epidermal naevi
Tags
  • somatic
Green Green List (high evidence)
FGFR3
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Epidermal naevi
  • Syringocystadenoma papilliferum
Tags
  • somatic
Green Green List (high evidence)
GNA11
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Extensive dermal melanocytosis
  • Phakomatosis pigmentovascularis
Tags
  • somatic
Green Green List (high evidence)
IDH2
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Maffucci syndrome
  • Ollier disease
Tags
  • somatic
Green Green List (high evidence)
MVD
1 review
1 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Genomics England PanelApp
  • NHS GMS
Phenotypes
  • Linear porokeratosis
  • Porokeratosis 7, multiple types, MIM# 614714
Tags

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